Abstract
A 4-year-old boy presented with a mucous membrane in the suprapubic region, a low-set umbilicus, and the typical musculoskeletal deformity seen in classic bladder exstrophy. The penis had a thin, rudimentary urethral plate on its dorsal surface. The main urethra was orthotopic and normal in size. Micturition was undisturbed and the child was continent of urine. Excision of the lesion and reconstruction of the suprapubic area with bilateral rhomboid skin flaps was curative. Pathologic examination of the removed specimen revealed transitional-cell epithelium and a tubular structure with an epithelial-cell lining resembling a deferential duct.
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Boemers, T.M.L., de Jong, T.P.V.M., Vegt, P.D.J. et al. Duplicate exstrophy. Pediatr Surg Int 10, 183–185 (1995). https://doi.org/10.1007/BF00171193
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DOI: https://doi.org/10.1007/BF00171193