Abstract
A rare case of congenital dumbbell neuroblastoma with paraplegia and sphincter involvement is described. Magnetic resonance imaging (MRI) clearly demonstrated both intraspinal and right paravertebral tumors in a patient who showed signs of paraplegia of the lower extremities at birth. The patient was treated by laminectomy and intraspinal tumor excision followed by retroperitoneal tumor excision. Mild chemotherapy consisting of low-dose cyclophosphamide and vincristine was carried out postoperatively for 6 months. Radiation therapy was not employed. At 13 months of age the patient showed no evidence of residual or recurrent tumor, and the paralysis of the right lower extremity was greatly improved.
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Uemoto, S., Tanaka, K., Inomata, Y. et al. Congenital dumbbell neuroblastoma. Pediatr Surg Int 5, 292–294 (1990). https://doi.org/10.1007/BF00169676
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DOI: https://doi.org/10.1007/BF00169676