Abstract
Three generations of a family with conjunctival xerosis, Rieger's anomaly (complete or incomplete) and arcus lipoides are described. The xerosis was found always to be accompanied by a Rieger anomaly, which had sometimes, but not always, been detected before. Independent heredity was not observed. In a number of cases the xerosis was bilateral and localised both temporally and nasally. The combination appears to be a stigma malformationis oculi. Correlation with a temporary vitamin A deficiency in early youth appears possible. At this age in such families caution is advisable in the administration of vitamin A inhibiting medicines such as steroids and neomycine.
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On the occasion of the Tropical Ophthalmology session of the Netherlands Ophthalmological Society, 1991, and 25 years after the presentation of Alkemade's paper on Xerosis-Aniridia at the session of 1966.
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De Keizer, R.J.W. Conjunctival xerosis, arcus lipoides and Rieger's disease. Doc Ophthalmol 78, 265–271 (1991). https://doi.org/10.1007/BF00165690
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DOI: https://doi.org/10.1007/BF00165690