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Extrauterine Endometrial Stromal Sarcoma: A Rare Entity

  • Urvashi MiglaniEmail author
  • Poonam Laul
  • Neeta Bindal
  • Puneet Chhibber
  • Pinkee Saxena
Case Report
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Abstract

ESS is a malignant mesenchymal tumor arising from the uterus. It rarely may occur in the extrauterine location where it is called endometrioid stromal sarcoma [also known as extrauterine endometrial stromal sarcoma (EESS)]. A patient Ms. X 20-year-old unmarried female presented to the outpatient department of Deen Dayal Upadhyay Hospital in July 2018 with the complaint of pain in lower abdomen for 1 week. MRI pelvis showed a large complex space occupying lesion with mixed cystic and soft tissue component measuring 7.2 by 8.3 by 6.8 cm showing non-homogeneous contrast enhancement. Per-operatively a highly vascular 10 by 20 cm cystic mass with necrotic and hemorrhagic areas was present which was densely adherent to omentum and mesentery. Uterus with bilateral tubes and ovaries was normal, and mass was arising from left round ligament. The final pathological diagnosis was given as stromal sarcoma of the round ligament with associated endometriosis.

Notes

Compliance with Ethical Standards

Conflict of interest

All authors declare that there is no conflict of interest.

Research Involving Human Participants and/or Animals

This article does not contain any studies with human or animal subjects.

References

  1. 1.
  2. 2.
    Masand RP, Euscher ED, Deavers MT, Malpica A. Endometrioid stromal sarcoma: a clinicopathologic study of 63 cases. Am J Surg Pathol. 2013;37(11):1635–47.  https://doi.org/10.1097/PAS.0000000000000083.CrossRefPubMedGoogle Scholar
  3. 3.
    Conklin CM, Longacre TA. Endometrial stromal tumors: the new WHO classification. Adv Anat Pathol. 2014;21(6):383–93.CrossRefGoogle Scholar
  4. 4.
    Puliyath G, Nair MK. Endometrial stromal sarcoma: a review of literature. Indian J Med Paediatr Oncol. 2012;33(1):1–6.CrossRefGoogle Scholar
  5. 5.
    Christopher V, Joseph A, Edward L. Extrauterine endometrial stromal sarcoma arising in peritoneal endometriosis. Am J Clin Pathol. 2016;146(Suppl_1):317.  https://doi.org/10.1093/ajcp/aqw159.088.CrossRefGoogle Scholar
  6. 6.
    Dupont NC, DiSaia PJ. Recurrent endometrial stromal sarcoma: treatment with a progestin and gonadotropin releasing hormone agonist. Sarcoma. 2010; 2010.Google Scholar

Copyright information

© Association of Gynecologic Oncologists of India 2019

Authors and Affiliations

  • Urvashi Miglani
    • 1
    • 2
    Email author
  • Poonam Laul
    • 1
  • Neeta Bindal
    • 1
  • Puneet Chhibber
    • 3
  • Pinkee Saxena
    • 1
  1. 1.Department of Obstetrics and GynecologyDeen Dayal Upadhyay HospitalHari Nagar, New DelhiIndia
  2. 2.GurgaonIndia
  3. 3.Department of SurgeryDeen Dayal Upadhyay HospitalHari NagarIndia

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