Rare Case Report of Primary Pseudomyxoma Ovarii with Disseminated Peritoneal Adenomucinosis
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Pseudomyxoma peritonei (PMP) is a poorly understood uncommon condition with an estimated incidence of one to two per million (worldwide) per year. It is characterized by the peritoneal deposition of mucinous implants, diffusely involving the peritoneal surfaces, most commonly of the appendix, and occasionally from the ovary, coupled with mucinous ascites. PMP associated with primary ovarian mucinous tumor was very rare. This is a case report of a 45-year-old female presented with large ovarian mass with gross ascites which was operated and diagnosed as primary atypical proliferative mucinous tumor with pseudomyxoma ovarii with disseminated peritoneal adenomucinosis.
KeywordsPseudomyxoma peritonei (PMP) Atypical proliferative mucinous tumor Pseudomyxoma ovarii Disseminated peritoneal adenomucinosis (DPAM)
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Conflict of interest
The authors declare that they have no conflict of interest.
This article does not contain any studies with human participants or animals performed by any of the authors as this is a retrospective case report only.
Informed consent from patient was taken.
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