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Rare Case Report of Primary Pseudomyxoma Ovarii with Disseminated Peritoneal Adenomucinosis

  • Renuka Gupta
  • Shruti Bhatia
  • Amit Gupta
  • Sheena Khetarpal Bajaj
Case Report
  • 9 Downloads

Abstract

Pseudomyxoma peritonei (PMP) is a poorly understood uncommon condition with an estimated incidence of one to two per million (worldwide) per year. It is characterized by the peritoneal deposition of mucinous implants, diffusely involving the peritoneal surfaces, most commonly of the appendix, and occasionally from the ovary, coupled with mucinous ascites. PMP associated with primary ovarian mucinous tumor was very rare. This is a case report of a 45-year-old female presented with large ovarian mass with gross ascites which was operated and diagnosed as primary atypical proliferative mucinous tumor with pseudomyxoma ovarii with disseminated peritoneal adenomucinosis.

Keywords

Pseudomyxoma peritonei (PMP) Atypical proliferative mucinous tumor Pseudomyxoma ovarii Disseminated peritoneal adenomucinosis (DPAM) 

Notes

Compliance with Ethical Standards

Conflict of interest

The authors declare that they have no conflict of interest.

Ethical Approval

This article does not contain any studies with human participants or animals performed by any of the authors as this is a retrospective case report only.

Informed Consent

Informed consent from patient was taken.

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Copyright information

© Association of Gynecologic Oncologists of India 2018

Authors and Affiliations

  1. 1.Department of Gynae-OncologyAction Cancer HospitalNew DelhiIndia
  2. 2.Department of RadiologyPentamed HospitalNew DelhiIndia
  3. 3.Action Cancer HospitalNew DelhiIndia

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