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American Journal of Clinical Dermatology

, Volume 16, Issue 4, pp 295–301 | Cite as

Poland’s Syndrome: A Concise Review of the Clinical Features Highlighting Associated Dermatologic Manifestations

  • Aria Vazirnia
  • Philip R. Cohen
Review Article

Abstract

Poland’s syndrome is a rare congenital condition characterized by absence of the pectoralis major muscle and a wide spectrum of associated ipsilateral chest wall and upper extremity anomalies. Associated dermatologic anomalies classically include pectoral and axillary alopecia, anhidrosis due to the absence of sweat glands, and deficiency in subcutaneous fat. Functional limitations are minimal, and thus surgical correction is primarily indicated for aesthetic purposes. Chest wall reconstruction typically involves transposition of a latissimus dorsi myocutaneous flap with or without a temporary subcutaneous tissue expander prior to surgical reconstruction. Using the PubMed database, a literature review was done on Poland’s syndrome. We summarize the key features of Poland’s syndrome, including the epidemiology, clinical presentation, pathogenesis, and management, and highlight the dermatologic associations reported in the literature.

Notes

Compliance with ethical standards

No funding was received for the preparation of this manuscript. Aria Vazirnia and Philip R. Cohen have no conflicts of interest to declare.

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Copyright information

© Springer International Publishing Switzerland 2015

Authors and Affiliations

  1. 1.School of MedicineUniversity of California San DiegoLa JollaUSA
  2. 2.Department of DermatologyUniversity of California San DiegoLa JollaUSA

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