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Perioperative Management of Pediatric Patients with Osteogenesis Imperfecta Undergoing Orthopedic Procedures

  • Pediatric Anesthesia (J Lerman, Section Editor)
  • Published:
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Abstract

Osteogenesis imperfecta (OI) is a predominantly autosomal dominant inherited condition involving connective tissue associated with not only bone fragility, but multi-system involvement with perioperative implications. The perioperative management of patients with OI undergoing orthopedic procedures is high risk for anatomical and physiological reasons. We performed a retrospective analysis of 13 years of data covering the perioperative management of 146 pediatric patients with OI for 280 operative procedures involving up to five bones each by two fellowship-trained pediatric orthopedic surgeons and a team of pediatric anesthesiologists. The purpose of the review was to describe updated perioperative anesthetic management based on over a decade of experience in a pediatric hospital specializing in the management of OI patients.

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Correspondence to Jessica K. Goeller.

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Conflict of Interest

Jessica K. Goeller, Cynthia A. Ferris, Paul W. Esposito, Maegen J. Wallace, Bridget A. Burke, and Cynthia R. Bailey declare they have no conflict of interest.

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This article does not contain any studies with human or animal subjects performed by any of the authors.

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This article is part of the Topical Collection on Pediatric Anesthesia

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Goeller, J.K., Esposito, P.W., Wallace, M.J. et al. Perioperative Management of Pediatric Patients with Osteogenesis Imperfecta Undergoing Orthopedic Procedures. Curr Anesthesiol Rep 7, 142–149 (2017). https://doi.org/10.1007/s40140-017-0207-8

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  • DOI: https://doi.org/10.1007/s40140-017-0207-8

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