Masticatory myorhythmia following pontine hemorrhage
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Myorhythmia is an involuntary regular, rhythmic movement, with a frequency of 1–3 Hz. In its most common form, it occurs in ocular and masticatory muscles (oculomasticatory myorhythmia, OMM), all or not in combination with skeletal muscles (oculofacial-skeletal myorhythmia, OFSM). When different body parts are involved, movements can either be synchronous or not. Masucci et al.  found clinicopathological correlates of limb myorhythmias in autopsy series, with involvement of the dentate nucleus, superior cerebellar peduncle, substantia nigra or inferior olive.
OMM or OFSM is most often associated with Whipple’s disease (WD) [2, 3, 4]. Neurologic manifestations emerge in 10–40 percent of patients with WD [5, 6]. OMM and OFSM occur in 8 percent of patients and are pathognomonic for this condition. Ocular myorhythmia consists mostly of convergent–divergent nystagmus, frequently in conjunction with supranuclear gaze palsy .
Other, less frequent disorders in which OMM or...
KeywordsInferior Olive Masticatory Muscle Sick Sinus Syndrome Superior Cerebellar Peduncle Brainstem Auditory Evoke Response
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