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Indian Pediatrics

, Volume 56, Issue 1, pp 69–71 | Cite as

Hyponatremic-Hypertensive Syndrome in Ovarian Paraganglioma

  • Manish KumarEmail author
  • Aashima Dabas
  • Vivek Manchanda
  • Nidhi Mahajan
  • Kaustuv Mitra
Case Report
  • 2 Downloads

Abstract

Objective

Hyponatremic-hypertensive syndrome (HHS) is characterized by combination of polyuria, polydipsia, hypertension, hyponatremia and hypokalemia in association with unilateral renal artery stenosis.

Case characteristics

A 10-year-old girl presented with polyuria, polydipsia, hypertension, hyponatremia, hypokalemia and proteinuria. Ultrasonography with doppler study revealed bilateral normal renal arteries. Completed tomography of abdomen detected a left adnexal mass, which was later confirmed as ovarian paraganglioma on histopathology.

Outcome

After tumor excision, polyuria subsided and blood pressure normalized.

Message

Hyponatremic-Hypertensive Syndrome does not always result from unilateral renal artery stenosis. High index of clinical suspicion with appropriate imaging technique may clinch rare endocrine causes of hypertension, like paraganglioma.

Keywords

Hypertension Nocturnal enuresis Paraneoplastic syndrome Polyuria 

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Copyright information

© Indian Academy of Pediatrics 2019

Authors and Affiliations

  • Manish Kumar
    • 1
    Email author
  • Aashima Dabas
    • 1
  • Vivek Manchanda
    • 2
  • Nidhi Mahajan
    • 3
  • Kaustuv Mitra
    • 1
  1. 1.Department of PediatricsChacha Nehru Bal Chikitsalaya, Geeta ColonyNew DelhiIndia
  2. 2.Department of Pediatric SurgeryChacha Nehru Bal ChikitsalayaNew DelhiIndia
  3. 3.Department of PathologyChacha Nehru Bal ChikitsalayaNew DelhiIndia

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