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XY Female with Complete Androgen Insensitivity Syndrome with Bilateral Inguinal Hernia

  • Rema V. Nair
  • S. Bhavana
Case Report

Introduction

The complete androgen insensitivity syndrome, previously called testicular feminization syndrome, is an X-linked recessive rare disorder. The individual is phenotypically female and genotypically male: a male pseudohermaphrodite. The individuals are reared as girls and the condition is suspected when the individual is evaluated for primary amenorrhea, infertility, or when unilateral/bilateral inguinal hernia is diagnosed in girls.

Case Report

A 30-year-old married lady presented to the gynecological OPD with complaints of swelling in the groin on both the sides for the past 4 months. The swelling increased on coughing, straining and reduced on lying down. There was no history suggestive of obstruction/irreducibility. She had not attained menarche. She was married to a widower for the past 8 years. The husband had 2 children from the first wife. They had no problems during sexual intercourse. She had 3 siblings, all of whom were married and had children.

On examination, she...

Keywords

Testosterone Inguinal Hernia Pubic Hair Secondary Sexual Character Androgen Insensitivity Syndrome 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

References

  1. 1.
    Oakes MB, Eyvazzadeh AD, Quint E, et al. Complete androgen insensitivity syndrome—a review. J Pediatr Adolesc Gynecol. 2008;21:305–10.CrossRefPubMedGoogle Scholar
  2. 2.
    Cools M, Drop SL, Wolffenbuttel KP, et al. Germ cell tumors in intersex gonad: old paths, new direction, moving frontiers. Endocr Rev. 2006;27:468–84.CrossRefPubMedGoogle Scholar

Copyright information

© Federation of Obstetric & Gynecological Societies of India 2013

Authors and Affiliations

  1. 1.Sree Mookambika Institute of Medical Sciences CampusVelayudhan Pillai Memorial Hospital ComplexKanyakumari DistrictIndia

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