Not All the Spindle Cell Tumors in Oral Cavity Are Sarcomatoid Squamous Cell Carcinoma
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Embryonal rhabdomyosarcoma (ERMS) is most common subtype of RMS arising from primitive embryonic skeletal-muscle cells. Hence, it can arise anywhere in the body, often in the sites where skeletal muscle is not usually found. RMS commonly occurs in the 1st decade of life in more than 50% of the cases. ERMS is extremely rare in adults. It commonly occurs in head and neck and genitourinary tract. Clinical manifestation varies depending upon mass effect and obstruction .
We reported a rare case of ERMS in a 48-year old male, presented as an ulcer over left buccal mucosa and rapidly progresses to a mass in left cheek, which was locally aggressive without distant metastasis. A detail histopathological examination with relevant IHC has to be performed in an atypical morphology at the odd site.
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