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Ewing’s Sarcoma with Extension into Superior Vena Cava and Right Atrium

  • Yukari Atsumi
  • Yuya Saito
  • Hiroshi Hataya
  • Ryuji Fukuzawa
  • Yuki Yuza
Case Report
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Abstract

Ewing sarcoma is rarely shown to develop this intravascular extension so the decision of the initial treatment is more difficult. We report a 7-year-old boy of this sarcoma with extension into superior vena cava (SVC) and right atrium (RA), who was successfully treated with initial surgery. Intravascular extension was observed from the azygous vein to SVC and finally RA. The removal of the intravascular extension was done, 7 days before chemotherapy was started. The initial surgery for the intravascular extension may have decreased a risk of pulmonary tumor embolism and this made the chemotherapy done safe in this patient.

Keywords

Ewing’s sarcoma Intravascular extension Tumor embolism Initial treatment 

Notes

Acknowledgments

We would like to thank the members of the department of cardiovascular surgery for their participation in the operation and we also thank Mr. James R. Valera for English proofreading.

Compliance with Ethical Standards

Conflict of Interest

The authors declare that they have no conflict of interest.

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Copyright information

© Indian Association of Surgical Oncology 2019

Authors and Affiliations

  • Yukari Atsumi
    • 1
  • Yuya Saito
    • 2
  • Hiroshi Hataya
    • 1
  • Ryuji Fukuzawa
    • 3
  • Yuki Yuza
    • 2
  1. 1.Department of General PediatricsTokyo Metropolitan Children’s Medical CenterTokyoJapan
  2. 2.Department of Hematology and OncologyTokyo Metropolitan Children’s Medical CenterTokyoJapan
  3. 3.Department of PathologyTokyo Metropolitan Children’s Medical CenterTokyoJapan

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