An Interesting Case of Fibromatosis of Neck with Review of Literature
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Fibromatosis is also known as desmoid tumour. It is a slow-growing and locally infiltrative disease caused by uncontrolled proliferation of fibrous tissue arising from deep musculoaponeurotic structures. It differs from fibrosarcoma in having low cellularity, infrequent mitoses, absence of necrosis, and not metastasising. Despite having benign histology, being locally aggressive it can cause significant morbidity .
Fibromatosis is a rare entity, representing only 0.03 % of all neoplasm in humans . It is classified according to its anatomical position into three subtypes namely abdominal, intra-abdominal, and extra-abdominal. Fibromatosis of the head and neck region comprises around 10 to 25 % of all cases of extra-abdominal fibromatosis . Attempts have been made to separate it from that arising from other parts of the body because of the unique clinical problems it can cause in relation to its critical anatomical position [3, 4, 5].
Though surgery is the main stay...
KeywordsTamoxifen Internal Jugular Vein Desmoid Tumour Neurovascular Bundle Tamoxifen Therapy
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