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Indian Journal of Surgical Oncology

, Volume 2, Issue 3, pp 212–214 | Cite as

A Rare Cause of Massive Lymphadenopathy

  • H. RajaEmail author
  • S. G. Subramanyam
  • Sridar Govindaraj
  • M. K. Babu
Case Report
  • 30 Downloads

Abstract

Rosai Dorfman Disease is a rare disease presenting mainly as painless enlargement of cervical lymph nodes. It is a benign disorder showing unique histological features characterized by reactive proliferation of sinus histiocytes. In 40% of cases, extranodal sites may be involved. The condition has to be differentiated from certain types of B cell lymphoma showing similar features. We report here a 17 year old male presenting with nodal and extranodal involvement of Rosai Dorfman Disease.

Keywords

Rosai dorfman disease Emperipolesis S – 100 protein 

Notes

Source of funding

Nil

Conflict of interest

Nil

References

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Copyright information

© Indian Association of Surgical Oncology 2011

Authors and Affiliations

  • H. Raja
    • 1
    Email author
  • S. G. Subramanyam
    • 2
  • Sridar Govindaraj
    • 2
  • M. K. Babu
    • 3
  1. 1.Department of SurgerySt. John’s Medical College HospitalBangaloreIndia
  2. 2.Department of SurgerySt. John’s Medical College HospitalBangaloreIndia
  3. 3.Department of PathologySt. John’s Medical College HospitalBangaloreIndia

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