Percutaneous transseptal mitral commissurotomy (PTMC) is the first line of treatment for selected patients of rheumatic mitral stenosis. Transseptal puncture is the most crucial step for performing a safe and successful PTMC. The distorted cardiac anatomy can lead to technical difficulties and increase the risk of serious complications. Isolated persistent left superior vena cava in a patient with visceroatrial situs solitus is rare. We report a case of successful PTMC in a patient with distorted anatomy due to aneurysmal dilatation of coronary sinus secondary to the persistent left superior vena cava, absent right superior vena cava and bulging interatrial septum.
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Srinivas, B.C., Singla, V., Reddy, B. et al. Percutaneous transseptal mitral commissurotomy in a patient with absent right superior vena cava and aneurysmally dilated coronary sinus. Cardiovasc Interv and Ther 28, 419–421 (2013) doi:10.1007/s12928-013-0196-6
- Mitral stenosis
- Persistent left superior vena cava
- Cardiac tamponade
- Septal puncture