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Nevoid-basal cell carcinoma syndrome: a case report and overview on diagnosis and management

  • Shridhar D. Baliga
  • Sanjay S. RaoEmail author
Case Report

Abstract

Nevoid Basal Cell Carcinoma Syndrome (NBCCS) is a rare condition characterized by varied clinical manifestations like multiple Basal Cell Carcinomas (BCC), multiple Keratocystic Odontogenic Tumours (KCOT), palmar and/or plantar pits and ectopic calcification of the falx cerebri, which are considered as the major criteria for diagnosis. The occurrence of jaw manifestations makes it an important diagnostic problem for oral and maxillofacial surgeons and often clinicians encounter this aspect which finally leads to the diagnosis of this syndrome. This paper reports a case of NBCCS and provides an overview on the diagnosis and management of this enigmatic entity.

Keywords

Nevoid basal cell carcinoma syndrome Gorlin-Goltz syndrome Keratocystic odontogenic tumour 

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Copyright information

© Springer 2009

Authors and Affiliations

  1. 1.Dept. of Oral and Maxillofacial SurgeryKLEVK Institute of Dental Sciences and HospitalBelgaumIndia
  2. 2.KLEVK Institute of Dental Sciences and HospitalBelgaumIndia

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