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Journal of Echocardiography

, Volume 10, Issue 3, pp 106–108 | Cite as

A case with double-chambered right ventricle and left ventricular–right atrial communication (Gerbode defect): potential pitfall for Eisenmenger syndrome

  • Demet Ozkaramanli GurEmail author
  • Ozcan Gur
  • Huseyin Goksuluk
  • Dervis Oral
Case Report
  • 114 Downloads

Abstract

The ventricular septal defect (VSD) can rarely be associated with other malformations such as double-chambered right ventricle (DCRV) in which hypertrophied muscle bundles divide the right ventricle into two chambers causing progressive obstruction (Mao et al., Asia Pac J Thorac Cardiovasc Surg 5:14–17, 1996). Most VSDs close spontaneously by apposition of the tricuspid leaflets, but the process is rarely disrupted, resulting in communication between left ventricle and right atrium called Gerbode defect [Cho et al., J Cardiovasc Ultrasound 19(3):148–151, 2011]. Hence, the Gerbode defect involves potential misinterpretation of its high-velocity shunt as pulmonary hypertension. Here we present a case with DCRV and Gerbode defect initially misdiagnosed to have Eisenmenger syndrome.

Keywords

Double-chambered right ventricle Gerbode defect Pulmonary hypertension Eisenmenger syndrome 

Notes

Conflict of interest

None.

Supplementary material

Supp.1: Parasternal short-axis view showing RV hypertrophy (AVI 3455 kb)

Supp.2: Parasternal short-axis view showing RV hypertrophy (AVI 3528 kb)

Supp.3: Apical 5-chamber view showing Gerbode defect and TR (AVI 3999 kb)

References

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Copyright information

© Japanese Society of Echocardiography 2012

Authors and Affiliations

  • Demet Ozkaramanli Gur
    • 1
    • 5
    Email author
  • Ozcan Gur
    • 2
  • Huseyin Goksuluk
    • 3
  • Dervis Oral
    • 4
  1. 1.Tekirdag State HospitalTekirdağTurkey
  2. 2.Department of Cardiovascular SurgeryNamık Kemal UniversityTekirdağTurkey
  3. 3.Eskisehir Sakarya HospitalEskisehirTurkey
  4. 4.Ankara Umut HospitalAnkaraTurkey
  5. 5.TekirdağTurkey

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