World Journal of Pediatrics

, Volume 9, Issue 2, pp 182–184 | Cite as

Blount disease in a case of Prader-Willi syndrome: why is it not as prevalent as in obesity without Prader-Willi syndrome?

  • Susan DulkaEmail author
  • Arabinda Kumar Choudhary
  • Sosamma Methratta
  • Kristine Fortuna
Case report



Prader-Willi syndrome (PWS) is a genetic disorder causing multisystem abnormalities with obesity. Obesity is a well established cause of Blount disease.


A 7-year-old girl with PWS presented with genu varum of the left knee with deformity of the proximal medial tibial condyle, which was consistent with Blount disease.


A lateral physeal stapling and subsequent osteotomy for the left proximal tibia and fibula were performed with improved anatomical alignment.


Blount disease has not been reported in the literature in association with PWS despite excessive obesity.

Key words

Blount disease genetics obesity Prader-Willi syndrome radiology 


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Copyright information

© Children's Hospital, Zhejiang University School of Medicine and Springer-Verlag Berlin Heidelberg 2013

Authors and Affiliations

  • Susan Dulka
    • 1
    Email author
  • Arabinda Kumar Choudhary
    • 1
  • Sosamma Methratta
    • 1
  • Kristine Fortuna
    • 2
  1. 1.Department of RadiologyPenn State/Milton S. Hershey Medical CenterHersheyUSA
  2. 2.Department of OrthopedicsPenn State/Milton S. Hershey Medical CenterHersheyUSA

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