World Journal of Pediatrics

, Volume 7, Issue 1, pp 79–82 | Cite as

Clinical outcome of nutrition-oriented intervention for primary intestinal lymphangiectasia

  • Qing-Ya Tang
  • Jie Wen
  • Jiang Wu
  • Ying Wang
  • Wei Cai
Brief Report

Abstract

Background

Primary intestinal lymphangiectasia (PIL) is a rare digestive disease and few studies have focused on the therapeutic effect in PIL patients. This study was undertaken to evaluate nutrition-oriented intervention in children with PIL.

Methods

Four children with PIL were studied. Their medical records were reviewed. Anthropometric measurements and blood tests were performed during a 8–18 month follow-up.

Results

During hospitalization, the 4 patients were subjected to diet intervention. Parenteral nutrition (PN) support was also given to 3 of them. Clinical symptoms and laboratory parameters of the patients were significantly improved at discharge. After discharge, the patients continued diet control, 2 of whom received intermittent PN support. The mean follow-up duration of the 4 patients was 13 months (range, 8–18 months) and they all kept in a stable condition without symptoms relapse. Weight, height and body mass index for age were normal during the follow-up, while total protein, albumin and immunoglobulin concentrations were still slightly below normal level.

Conclusions

Nutrition therapy is effective as a valid and safe therapeutic management for PIL patients. No growth retardation was observed in the 4 children after the therapy, but they are still at risk of nutrient malabsorption. Therefore, they need long-term, regular monitoring and intensive nutritional care.

Key words

nutrition assessment nutrition intervention primary intestinal lymphangiectasia 

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Copyright information

© Children's Hospital, Zhejiang University School of Medicine and Springer-Verlag Berlin Heidelberg 2011

Authors and Affiliations

  • Qing-Ya Tang
    • 1
  • Jie Wen
    • 1
  • Jiang Wu
    • 1
  • Ying Wang
    • 1
  • Wei Cai
    • 2
    • 3
  1. 1.Clinical Nutrition CenterShanghai Jiao Tong University, School of Medicine, Xin Hua HospitalShanghaiChina
  2. 2.Department of Pediatric SurgeryShanghai Jiao Tong University, School of Medicine, Xin Hua Hospital, Shanghai Institute of Pediatric ResearchShanghaiChina
  3. 3.Department of Pediatric Surgery, Xin Hua Hospital, School of MedicineShanghai Jiao Tong UniversityShanghaiChina

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