Hepatosplenic T-Cell Lymphoma

  • Fahad I. Alsohaibani
  • Maheeba A. Abdulla
  • Mousa M. Fagih
Case Report

Abstract

We report an uncommon case of 38-year-old male patient with Hepatosplenic T-Cell lymphoma (HSTCL) which is a rare aggressive form of Peripheral T-Cell lymphoma that is characterized by primary extranodal disease with malignant T-cell proliferation in the liver, spleen, and bone marrow. Our patient presented with progressive painless jaundice, weight loss and massive hepatosplenomegaly. The diagnosis was challenging as he required an extensive investigations that ultimately showed the characteristic clinical, histopathologic, and cytogenetic features of hepatosplenic T-cell lymphoma.

Keywords

Hepatosplenic Lymphoma Hepatosplenomegaly 

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Copyright information

© Indian Society of Haematology & Transfusion Medicine 2011

Authors and Affiliations

  • Fahad I. Alsohaibani
    • 1
  • Maheeba A. Abdulla
    • 1
  • Mousa M. Fagih
    • 1
  1. 1.Section of Gastroenterology, Department of Medicine (MBC-46)King Faisal Specialist Hospital & Research Centre (KFSH&RC)RiyadhSaudi Arabia

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