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Indian Journal of Surgery

, Volume 75, Supplement 1, pp 460–462 | Cite as

Persistent Müllerian Duct Syndrome: a Case Report

  • Vijaya Patil
  • Sunilkrishna Muktinaini
  • Rashmi Patil
  • Ashish Verma
Case Report

Abstract

Persistent Müllerian duct syndrome is a rare form of internal male pseudohermaphroditism caused by defects in synthesis or action of Müllerian-inhibiting factor, due to which Müllerian duct derivatives, such as uterus, fallopian tube, and upper vagina, are normally present in 46XY males. Here, we report a 26-year-old male with right-sided obstructed inguinal hernia with left undescended testis. On exploration, hernial sac containing bowel loops, uterus with fallopian tubes, upper vagina, and testes were present.

Keywords

Persistent Müllerian duct syndrome Transverse testicular ectopia Hernia uteri inguinale 

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Copyright information

© Association of Surgeons of India 2013

Authors and Affiliations

  • Vijaya Patil
    • 1
  • Sunilkrishna Muktinaini
    • 2
  • Rashmi Patil
    • 2
  • Ashish Verma
    • 2
  1. 1.Department of SurgeryB.L.D.E.U.’s Shri B.M. Patil Medical College & Research CentreBijapurIndia
  2. 2.Department of General SurgeryB.L.D.E.U.’s Shri B.M. Patil Medical College & Research CentreBijapurIndia

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