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2019 Updated diagnostic criteria and disease severity classification for TAFRO syndrome

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  1. 1.

    Masaki Y, Kawabata H, Fujimoto S, Kawano M, Iwaki N, Kotani T, et al. Epidemiological analysis of multicentric and unicentric Castleman disease and TAFRO syndrome in Japan. J Clin Exp Hematop. 2019 (in press)

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    Iwaki N, Fajgenbaum DC, Nabel CS, Gion Y, Kondo E, Kawano M, et al. Clinicopathologic analysis of TAFRO syndrome demonstrates a distinct subtype of HHV-8-negative multicentric Castleman disease. Am J Hematol. 2016;91:220–6.

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    Fujimoto S, Sakai T, Kawabata H, Kurose N, Yamada S, Takai K, et al. Is TAFRO syndrome a subtype of idiopathic multicentric Castleman disease? Am J Hematol. 2019;94:975–83.

  4. 4.

    Masaki Y, Kawabata H, Takai K, Kojima M, Tsukamoto N, Ishigaki Y, et al. Proposed diagnostic criteria, disease severity classification and treatment strategy for TAFRO syndrome, 2015 version. Int J Hematol. 2016;103(6):686–92.

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This study was supported in part by grants from the Ministry of Health, Labor and Welfare, Japan (H29 Nanchi, etc. (Nan)-General-019, H27-28 Nanchi, etc. (Nan)-General-002 and -008), and by the Japanese Ministry of Education, Culture, Sports, Science and Technology (Grant No.17591060 and 15K09510), the Kanazawa Medical University Research Foundation (Grant Nos. S2004-16 and S2007-5), Grant for Assist KAKEN from Kanazawa Medical University (Grant No. K2011-7), Grant for Project Research from High-Tech Research Center of Kanazawa Medical University (Grant No. H2011-11) and Grant for Alumni Research(A) from Kanazawa Medical University (AR2012-06).

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Correspondence to Yasufumi Masaki.

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Conflict of interest

YM has received research grants from Kyowa Hakko Kirin Pharma, Astellas Pharma, Eisai Pharma, Ono Pharma, Pfizer Pharma, Asahi Kasei Pharma, MSD Pharma, Daiichi-Sankyo Pharma, Taisho Pharma, Taiho Pharma, Takeda Pharma, Chugai Pharma, Teijin Pharma, Nippon Kayaku, and Mochida Pharma, outside the submitted work. All other authors have no conflicts of interest.

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Masaki, Y., Kawabata, H., Takai, K. et al. 2019 Updated diagnostic criteria and disease severity classification for TAFRO syndrome. Int J Hematol 111, 155–158 (2020). https://doi.org/10.1007/s12185-019-02780-1

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