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Low-Grade Fibromyxoid Sarcoma of the External Auditory Canal: A Rare Pathology and Unusual Location

  • Kalpana Kumari
  • Ramya Thota
  • Heera Lal Chaudhary
  • Mehar C. Sharma
  • Alok Thakar
  • Geetika SinghEmail author
Case Report
  • 25 Downloads

Abstract

Low-grade fibromyxoid sarcoma (LGFMS) is an enigmatic soft tissue tumor. It frequently presents as a deeply seated mass in the proximal extremities and trunk. Superficial LGFMSs of the head and neck are exceedingly rare. Hyalinizing spindle cell tumor with giant rosettes (HSTGR) is an entity considered to be on the histologic spectrum of LGFMS. We present a case of a 44-year-old female who presented with a superficial, polypoid mass of the external auditory meatus. Microscopic examination revealed the classic histologic features of HSTGR. To our knowledge, this case is the first described at this extremely unusual location. Identification and reporting of such unusual cases is important to understand and compare the behavior of superficial LGFMS to that of the more common deeply seated tumors.

Keywords

Low-grade fibromyxoid sarcoma Hyalinizing spindle cell tumor with giant rosettes Superficial External auditory meatus 

Notes

Compliance with Ethical Standards

Conflict of interest

All authors declare no potential conflicts of interest (financial or non-financial).

Informed Consent

Informed consent was obtained from the patient. As article is in the form of case report with maintained patient anonymity, ethical clearance was not required.

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Copyright information

© Springer Science+Business Media, LLC, part of Springer Nature 2019

Authors and Affiliations

  1. 1.Department of PathologyAll India Institute of Medical SciencesNew DelhiIndia
  2. 2.Department of OtorhinolaryngologyAll India Institute of Medical SciencesNew DelhiIndia
  3. 3.Department of RadiologyAll India Institute of Medical SciencesNew DelhiIndia
  4. 4.Department of PathologyAll India Institute of Medical SciencesNew DelhiIndia

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