Head and Neck Pathology

, Volume 7, Issue 3, pp 280–284 | Cite as

Fibromatosis Arising in Association with Neuromuscular Hamartoma of the Mandible

  • Leena Yaseen Taher
  • Muhammad Saleem
  • Suresh Velagapudi
  • Anas Dababo
Case Report


Aggressive fibromatosis is a benign but locally-aggressive tumor, which most often affects the muscles of the shoulder, the pelvic girdle, and the thigh. It usually affects adolescents and young adults. Desmoplastic fibroma, considered the bone counterpart of soft tissue fibromatosis, is a rare tumor that usually affects the metaphyseal or diaphyseal portions of long bones or, less commonly, the jaw. Neuromuscular hamartoma, a rare developmental lesion composed of mature elements of both striated muscle and nerve, is usually diagnosed in infants and children and affects large nerve trunks. Rarely, it can affect the head and neck region. Occasional cases showing an association between aggressive fibromatosis and neuromuscular hamartoma have been reported in the literature. Here we present a unique case of an adult patient with desmoplastic fibroma of the mandible in association with neuromuscular hamartoma.


Neuromuscular hamartoma Desmoplastic fibroma Aggressive fibromatosis Mandible 


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Copyright information

© Springer Science+Business Media New York 2013

Authors and Affiliations

  • Leena Yaseen Taher
    • 1
    • 4
  • Muhammad Saleem
    • 2
  • Suresh Velagapudi
    • 2
  • Anas Dababo
    • 3
  1. 1.Department of PathologyTaibah UniversityAl-MadinaSaudi Arabia
  2. 2.Department of Otorhinolaryngology Head and Neck SurgeryKing Faisal Specialist Hospital and Research CentreRiyadhSaudi Arabia
  3. 3.Department of PathologyKing Faisal Specialist Hospital and Research CentreRiyadhSaudi Arabia
  4. 4.Department of Pathology (32)College of Medicine and King Khaled University HospitalRiyadhSaudi Arabia

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