The Indian Journal of Pediatrics

, Volume 84, Issue 3, pp 211–215 | Cite as

Ankle-Foot Orthosis in Duchenne Muscular Dystrophy: A 4 year Experience in a Multidisciplinary Neuromuscular Disorders Clinic

  • Anupam Gupta
  • Atchayaram Nalini
  • Shanti Prakash Arya
  • Seena Vengalil
  • Meeka Khanna
  • Rashmi Krishnan
  • Arun B. Taly
Original Article
  • 308 Downloads

Abstract

Objective

To assess Ankle-Foot-Orthosis (AFO) requirement and ambulation in Duchenne Muscular Dystrophy (DMD) patients seen over a period of 4 y at a multi-disciplinary Neuromuscular disorders clinic (NMD).

Methods

A study was conducted in university quaternary research hospital with DMD patients confirmed by MLPA (multiplex ligation – dependent probe amplification) method and were evaluated between January 2012 and December 2015. Their ambulatory status, detailed neurological and functional status were recorded. Requirement of AFOs was determined and provided.

Results

In total 126 DMD children reported to the NMD clinic. Mean age at presentation was 7.6 y (range 2 to12 y, SD 2.1). Mean duration of illness at first evaluation was 3.4 y (range 0.5 to 10 y, SD 2.0). AFO’s were advised at a mean age of 8.5 y (range 7 to 12 y, SD 1.8). Fifty-nine patients were advised AFO as resting or walking splint. At last follow-up 113 patients were still ambulatory whereas 13 had become wheel chair bound. Out of 59 patients, 48 were still wearing AFOs and the remaining discontinued AFOs for various reasons.

Conclusions

Children with DMD require wearing of AFOs as resting or walking splint, mostly in first or early second decade of life. As there is some gap between onset of clinical signs and requirement of orthosis, follow-up preferably at a multidisciplinary clinic at regular intervals is desirable for timely intervention in the form of AFOs or other splints to prolong ambulatory status in these patients.

Keywords

Duchenne muscular dystrophy Ankle-foot-orthosis Locomotion 

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Copyright information

© Dr. K C Chaudhuri Foundation 2016

Authors and Affiliations

  • Anupam Gupta
    • 1
  • Atchayaram Nalini
    • 2
  • Shanti Prakash Arya
    • 1
  • Seena Vengalil
    • 2
  • Meeka Khanna
    • 1
  • Rashmi Krishnan
    • 1
  • Arun B. Taly
    • 1
    • 2
  1. 1.Department of Neurological RehabilitationNational Institute of Mental Health & Neuro Sciences (NIMHANS)BengaluruIndia
  2. 2.Department of NeurologyNational Institute of Mental Health & Neuro Sciences (NIMHANS)BengaluruIndia

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