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The Indian Journal of Pediatrics

, Volume 82, Issue 3, pp 292–293 | Cite as

Seckel Syndrome with Severe Sinus Bradycardia

  • Chandramohan Ramasamy
  • Santhosh Satheesh
  • Raja SelvarajEmail author
Clinical Brief
  • 168 Downloads

Abstract

Seckel syndrome is an uncommon form of microcephalic dwarfism. The authors report a young boy with Seckel syndrome who presented with severe sinus bradycardia with symptoms of syncope and presyncope. Implantation of a permanent pacemaker was necessary in view of the severe symptoms. Although uncommon, cardiac abnormalities have been rarely reported in Seckel syndrome. This is the one of the few reports of rhythm abnormalities in this condition.

Keywords

Seckel syndrome Arrhythmia Sinus bradycardia Pacemaker 

Notes

Contributions

CR: Conceived the report and drafted the manuscript; SS: Contributed to conception and design, helped in revising the manuscript; RS: Revised the manuscript, prepared figures and oversaw the whole report. RS will act as guarantor for this paper.

Conflict of Interest

None.

Source of Funding

None.

References

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Copyright information

© Dr. K C Chaudhuri Foundation 2014

Authors and Affiliations

  • Chandramohan Ramasamy
    • 1
  • Santhosh Satheesh
    • 1
  • Raja Selvaraj
    • 1
    Email author
  1. 1.Department of CardiologyJawaharlal Institute of Postgraduate Medical Education and ResearchPuducherryIndia

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