Congenital Hepatic Arteriovenous Malformation Presenting with Severe Persistent Pulmonary Hypertension
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Abstract
Congenital hepatic arteriovenous malformation is a rarely seen vascular malformation with persistent pulmonary hypertension in neonates. The authors report a full-term female newborn presenting with intractable heart failure and respiratory distress soon after birth. Investigation by echocardiography showed severe persistent pulmonary hypertension of the newborn and patent ductus arteriosus. The hepatic angiogram revealed congenital hepatic arteriovenous malformation; therefore, secondary pulmonary artery hypertension complicated with ‘steal’ phenomenon was conclusively diagnosed.
Keywords
Arteriovenous malformation Embolization Hepatic Neonate Pulmonary hypertension Respiratory distressAbbreviations
- AVM
Arteriovenous malformation
- BRCM
Below right costal margin
- CHF
Congestive heart failure
- CT
Computed tomography
- HAVM
Hepatic arteriovenous malformation
- PBF
Pulmonary blood flow
- PPHN
Persistent pulmonary hypertension of the newborn
- PVR
Pulmonary vascular resistance
Notes
Acknowledgements
The authors thank the International Affairs Unit for helping with English.
Contributions
AT; Acquisition of data and manuscript preparation, PC,WJ,SD,AT;Neonatal assessment, SK;Pediatric radiologist; KH; Interventional radiologist, AT;Analysis and interpretation of data, PC,WJ,SD,AT;Final approval.
Conflict of Interest
None.
Role of Funding Source
None.
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