The Indian Journal of Pediatrics

, Volume 78, Issue 8, pp 1010–1012 | Cite as

Cardiopulmonary Arrest Caused by Craniometaphyseal Dysplasia

  • Ayako Chida
  • Youichi Yanagawa
  • Hiroshi Matsumoto
  • Shigeaki Nonoyama
Clinical Brief
First Online:
Received:
Accepted:

Abstract

Craniometaphyseal dysplasia is a rare congenital disorder that can cause craniofacial skeleton and tubular bone anomalies. A 7-month-old girl, with congenital facial palsy, mouth breathing, and nasal obstruction, was brought to the hospital because she suffered sudden cardiopulmonary arrest. Computed tomography showed bony narrowing of the choanae. The diagnosis was cardiopulmonary arrest triggered by asphyxia caused by severe choanal stenosis. She showed hypoxic encephalopathy and underwent a tracheotomy and an operation to enlarge choanae. When a neonate or young infant shows signs of nasal obstruction, physicians should aggressively search for and consider the possibility of choanal atresia or severe stenosis.

Keywords

Choanal stenosis Craniometaphyseal dysplasia Cardiopulmonary arrest Mouth breathing 
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Copyright information

© Dr. K C Chaudhuri Foundation 2011

Authors and Affiliations

  • Ayako Chida
    • 1
  • Youichi Yanagawa
    • 2
  • Hiroshi Matsumoto
    • 1
  • Shigeaki Nonoyama
    • 1
  1. 1.Department of PediatricsNational Defense Medical College (NDMC)SaitamaJapan
  2. 2.Department of Traumatology and Critical Care MedicineNDMCSaitamaJapan

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