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The Indian Journal of Pediatrics

, Volume 78, Issue 6, pp 737–739 | Cite as

Gorham-Stout Syndrome with Chylothorax in a Six-Year-Old Boy

  • Murat DeveciEmail author
  • Nagihan İnan
  • Funda Çorapçıoğlu
  • Gülşen Ekingen
Clinical Brief

Abstract

Gorham-Stout syndrome, also called “disappearing bone disease, diffuse cystic angiomatosis of bone, disseminated lymphangiomatosis, Gorham’s vanishing bone disease, phantom bone disease or idiopathic massive osteolysis, is a rare disease of unknown etiology and pathogenesis. It is characterized by rapidly progressive localized massive osteolysis associated with proliferation of vascular structures of benign origin in which the absence of new bone formation is representative. When it is complicated by chylothorax, the prognosis is poor. The authors report a 6-year-old boy with Gorham-Stout syndrome who presented with pleural effusion showing features of chylothorax, who responsed poorly to currently available therapeutic modalities.

Keywords

Gorham-Stout syndrome Chylothorax Osteolysis 

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Copyright information

© Dr. K C Chaudhuri Foundation 2010

Authors and Affiliations

  • Murat Deveci
    • 1
    Email author
  • Nagihan İnan
    • 2
  • Funda Çorapçıoğlu
    • 3
  • Gülşen Ekingen
    • 4
  1. 1.Department of Pediatric CardiologyEge University Faculty of MedicineBornova-IzmirTurkey
  2. 2.Department of RadiologyKocaeli University Faculty of MedicineKocaeliTurkey
  3. 3.Department of Pediatric OncologyKocaeli University Faculty of MedicineKocaeliTurkey
  4. 4.Department of Pediatric SurgeryKocaeli University Faculty of MedicineKocaeliTurkey

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