Adult Langerhans cell histiocytosis and sclerosing cholangitis: a case report and review of the literature
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- Hatemi, I., Baysal, B., Senturk, H. et al. Hepatol Int (2010) 4: 653. doi:10.1007/s12072-010-9205-3
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Sclerosing cholangitis is a rare complication of Langerhans cell histiocytosis in children which can result in liver failure. This combination is even rarer in adults.
We report a 65-year-old female who developed sclerosing cholangitis 4 years after the diagnosis of Langerhans cell histiocytosis.
Sclerosing cholangitis caused by Langerhans cell histiocytosis is a rare condition in the adult population, but it has a high mortality. There is no definitive therapy other than liver transplantation. The long-term efficacy of liver transplantation remains unknown.