The Rosai–Dorfman Disease: A Differential Diagnosis in Cervical Swelling

  • Ashutosh SinghEmail author
  • Surendra Kumar Kanaujiya
Clinical Report


Rosai–Dorfman disease also known as sinus histiocytosis with massive lymphadenopathy is a rare benign disorder of unknown etiology. It is a benign condition which causes significant cervical lymphadenopathy in children and young adults. These cases are frequently misdiagnosed as lymphoma, and thus it is important to distinguish Rosai–Dorfman disease from other causes of neck swelling because of different treatment modalities. We report here a case of Rosai–Dorfman disease presenting with massive right cervical lymphadenopathy.


Massive lymphadenopathy Rosai–Dorfman disease Sinus histiocytosis 


Compliance with Ethical Standards

Conflict of interest

The authors declare that they have no competing interests.

Ethical Approval

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

Informed Consent

Informed consent was obtained from all individual participant included in the study.


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Copyright information

© Association of Otolaryngologists of India 2017

Authors and Affiliations

  1. 1.G.S.V.M. Medical CollegeKanpurIndia

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