Abstract
Pleuropulmonary blastoma (PPB) is a rare, malignant tumor of the lung and is the most common primary pulmonary malignancy in children. Here, we report a case of a boy who was diagnosed with type I regressed PPB after being mislabeled with congenital pulmonary malformation. A 10-year-old boy presented to our hospital with a history of worsening dyspnea. Since birth, his clinical status and radiographic images were concerning for congenital lobar emphysema that was managed conservatively. A chest computed tomography (CT) scan confirmed the persistence of a large cystic lesion and a diagnostic and therapeutic cystectomy was performed. Microscopic examination confirmed the presence of PPB type Ir. Patient was managed surgically alone with no added chemotherapy, as there was no overall survival benefit. PPB Ir has an overall favorable clinical outcome. Limited follow-up data are available due to the rarity of the lesion and the overlap with other congenital cystic lung malformations.
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Acknowledgments
We are grateful for the parents for allowing us to report the case. The authors would like to thank doctor Mohamed Issa Tawil for providing us with the radiology images and doctor Saja Fetyan for her help during the writing process.
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Al Absi, H.S., Konstantinopoulou, S., Al Junaibi, A.A. et al. Type I regressed pleuropulmonary blastoma in a 10-year-old boy. Indian J Thorac Cardiovasc Surg 35, 579–583 (2019). https://doi.org/10.1007/s12055-019-00814-1
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DOI: https://doi.org/10.1007/s12055-019-00814-1