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Left parasternal approach for Bentall procedure in a patient of Marfan syndrome with severe pectus excavatum

  • Pankaj Aggarwal
  • Sachin Mahajan
  • Siddharth Garg
Case report

Abstract

Annuloaortic ectasia with ascending aortic aneurysm with severe aortic regurgitation with severe left ventricular dysfunction is a serious condition especially in patients with Marfan syndrome (MFS) simultaneously having severe pectus excavatum (PE) deformity. We report our left parasternal approach in such patient in whom median sternotomy was not feasible. We achieved excellent exposure of dislocated heart and great vessels enabling Bentall procedure. Since patient did not consent for combined correction of chest wall deformity, we plan to undertake it later. Therefore, we conclude that left parasternal approach is feasible for standard aortic root replacement surgery in severe PE.

Keywords

Left parasternal approach Annuloaortic ectasia Bentall procedure 

Notes

Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflict of interest.

Ethical approval

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

Informed consent

Informed consent was obtained from patient included in the study.

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Copyright information

© Indian Association of Cardiovascular-Thoracic Surgeons 2017

Authors and Affiliations

  • Pankaj Aggarwal
    • 1
  • Sachin Mahajan
    • 1
  • Siddharth Garg
  1. 1.Department of CTVSPGIMERChandigarhIndia

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