A rare case report of mucoepidermoid carcinoma arising in congenital cystic adenomatoid malformation

  • Narasimhan Meenakshi
  • Ramachandran Krishnan Sasankh
  • Kumarasamy Thiruppathi
  • Kabirdoss Rajarajan
Case Report
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Abstract

We report a case of 19 years old male presenting with cough and hemoptysis of 10 days duration, chest x-ray showed left hilar enlargement. Computed Tomograpy Scan-Chest showed left hilar adenopathy with segmental collapse in left upper lobe. Fibreoptic bronchoscopy revealed growth partially occluding the left main bronchus. Endobronchial biopsy showed features suggestive of squamous cell carcinoma. Left pneumonectomy with lymph node dissection done. Histopathological examination showed features of Congenital Cystic Adenomatoid Malformation (CCAM) with focus of low grade mucoepidermoid carcinoma. The literature data confirm that CCAM can rarely undergo malignant transformation and because of the risk of malignant change, early removal of CCAM of lung is advisable.

Keywords

Computed tomography Bronchoscopy Pneumonectomy 
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Copyright information

© Indian Association of Cardiovascular-Thoracic Surgeons 2012

Authors and Affiliations

  • Narasimhan Meenakshi
    • 1
  • Ramachandran Krishnan Sasankh
    • 2
  • Kumarasamy Thiruppathi
    • 1
  • Kabirdoss Rajarajan
    • 1
  1. 1.Institute of Thoracic MedicineChennaiIndia
  2. 2.Department of Cardiothoracic SurgeryRajiv Gandhi Government General Hospital and Madras Medical CollegeChennaiIndia

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