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Malignant Spindle Cell Neoplasm of Intestine: a Rare Case Report

  • Jyotsna Naresh Bharti
  • Kavita SharmaEmail author
  • Subhash Soni
  • Deepsikha Dharamsaktu
Case Report
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Introduction

Gastrointestinal stromal tumors (GISTs) are uncommon tumors accounting for 1% of all gastrointestinal tract (GIT) neoplasms [1]. GISTs are rare form of soft tissue sarcoma of the GIT. Two thirds of the GISTs are located in stomach while one fourth develops in the small intestine [2, 3]. The incidence of the GIST is very low, that is, 2 in 1,00,000, while jejunal GIST is extremely rare accounting for 0.1–3% of all GIT tumors [4]. The present discussion is limited to the small percentage which is found arising primarily from mesodermal tissue, the so-called spindle-cell tumors [2, 3, 4]. The typical subdivisions of this group—the neurinoma or neurofibroma, the leiomyoma, and the fibroma—are histologically well defined. Gastrointestinal stromal tumors (GISTs) are the most common mesenchymal tumors of the stomach with an incidence of 33–63% [1, 5, 6].

Case Presentation

A 66-year-old male presented with complains of bleeding per rectum on and off for a period of 2 years. On...

Notes

Compliance with Ethical Standards

Conflict of Interest

NIL

References

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Copyright information

© Springer Science+Business Media, LLC, part of Springer Nature 2019

Authors and Affiliations

  1. 1.Department of PathologyAll India Institute of Medical SciencesJodhpurIndia
  2. 2.JodhpurIndia

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