A Case Report of a Primary Neuroendocrine Tumour of the Proximal Common Bile Duct

  • Mohamed Ali ChaouchEmail author
  • Mohamed Wejih Dougaz
  • Wael Ferjaoui
  • Esma Leila Gouta
  • Ramzi Nouira
  • Ibtissem Bouasker
  • Chadli Dziri
Case Report


A neuroendocrine tumour (NET) of the extrahepatic bile ducts is rare accounting 0.2 to 2% of all gastrointestinal carcinoid tumours [1]. Localization in the proximal part of the common bile duct (CBD) is rare [2]. Signs and symptoms are not specific, may be similar to bile duct stones. Preoperative diagnosis is difficult [3]. The aim of this report is to describe a CBD NET not diagnosed preoperatively to highlight the difficulties encountered in this kind of situation despite the contribution of imaging in this rare localization: the junction of the common hepatic duct and cystic duct.

Case Report

A 39-year-old man with no past medical history consulted for epigastric pain, jaundice and weight loss in the last 8 months. He did not present hormone-related symptoms such as flushing, stomach aches, diarrhoea or hypoglycemia. Physical exam was normal. Laboratory data showed mild elevation of serum total bilirubin (57.7 μmol/l), direct bilirubin (38.4 μmol/l), γ-glutamyl-transf...


Compliance with Ethical Standards

Conflict of Interest

The authors declare that they have no conflicts of interest.


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© Springer Science+Business Media, LLC, part of Springer Nature 2019

Authors and Affiliations

  1. 1.Department of surgery BCharles Nicolle HospitalTunisTunisia

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