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Bile Duct Hamartoma Mimicking Liver Metastasis in Suspected Porcelain Gallbladder: a Case Report

  • Gautham Krishnamurthy
  • Harjeet Singh
  • Sravya Deepika Ganti
  • Ganga Ram VermaEmail author
Case Report
  • 8 Downloads

Introduction

Bile duct hamartoma, also called as von Mayenburg complexes, are rare hepatic lesions arising due to a disturbance in the ductal plate remodeling during embryogenesis. [1] The incidence is estimated to be 0.69 to 5.6% in autopsy series. [2, 3] Solitary multicystic bile duct hamartoma are extremely rare and till 2014 only ten cases have been reported in the English literature. [4] We report a case of incidental solitary multicystic biliary hamartoma in a patient undergoing laparoscopic cholecystectomy for suspected porcelain gallbladder.

Case Report

A 45-year-old female presented with bilateral flank pain and mild right hypochondrial pain for 4 months. She was detected to have bilateral renal calculi and porcelain gallbladder on sonography and non-contrast computed tomography (Fig.  1a). Clinical examination was unremarkable. On reevaluation with ultrasonography, the presence of porcelain gallbladder was confirmed along with tiny renal calculi. Hemogram, liver function...

Notes

Compliance with Ethical Standards

Conflict of Interest

The authors declare that they have no conflicts of interest.

Informed Consent

Informed consent was obtained from the patient regarding the usage of her information for the purpose of publication.

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© Springer Science+Business Media, LLC, part of Springer Nature 2019

Authors and Affiliations

  1. 1.Department of General SurgeryPost Graduate Institute of Medical Education and ResearchChandigarhIndia

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