Undifferentiated Embryonal Sarcoma of the Liver: a Great Masquerader

  • Alexander M. SyEmail author
  • Maureen Whitsett
  • Xiaodong Li
  • Neil D. Theise
  • Nabil N. Dagher
  • Sonja Olsen
Case Report


Undifferentiated embryonal sarcoma of the liver (UESL) is a rare primary tumor in adults. Misdiagnosis is largely due to its infrequency in adult patients, the absence of specific diagnostic blood tests, and lack of classic radiologic findings. This is a case of a 33-year-old Asian male who presented with a painful hepatic mass and fevers thought initially to be infectious, but later diagnosed as UESL which was successfully resected.


A 33-year-old male with known glucose-6-phosphate dehydrogenase deficiency was admitted for worsening right upper quadrant abdominal pain, nausea, and vomiting of 1 day duration in the setting of subacute weight loss, malaise, and intermittent fevers as high as 103.7 °F at home. Three weeks prior to admission, in addition to these symptoms, he developed new right scapular pain which he treated with ibuprofen and acetaminophen. One day prior to admission, he experienced sharp, right upper quadrant pain as well as an episode of non-bilious,...


Compliance with Ethical Standards

Conflict of Interest

The authors declare that they have no conflict of interest.

Informed Consent

Informed consent was taken from the patient.


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© Springer Science+Business Media, LLC, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Division of Gastroenterology, Hepatology and NutritionNYU Winthrop HospitalMineolaUSA
  2. 2.Division of Gastroenterology and HepatologyNYU Langone Medical CenterNew York CityUSA
  3. 3.Department of PathologyNYU Langone Medical CenterNew York CityUSA
  4. 4.NYU Langone Transplant InstituteNYU Langone Medical CenterNew York CityUSA
  5. 5.Division of Transplant HepatologyNYU Langone Medical CenterNew York CityUSA

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