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Current Rheumatology Reports

, 16:465 | Cite as

Amyopathic Dermatomyositis: Definitions, Diagnosis, and Management

  • Elizabeth E. Bailey
  • David F. Fiorentino
Inflammatory Muscle Disease (RG Cooper, Section Editor)
Part of the following topical collections:
  1. Topical Collection on Inflammatory Muscle Disease

Abstract

Amyopathic dermatomyositis can be a challenging diagnosis because patients lack traditional muscle findings. “Clinically amyopathic” dermatomyositis (CADM) accounts for the presence of subclinical muscle disease in some of these patients. These patients represent a substantial minority of dermatomyositis cases and have similar co-morbidities to “classic” dermatomyositis patients, including interstitial lung disease and malignancy. Clinically amyopathic dermatomyositis patients should not be considered as a distinct clinical entity from “classic” dermatomyositis, as they share antibody sub-types and associated co-morbidities, likely representing clinical spectrum of a common disease. It is essential for the clinician to be familiar with the clinical presentation of clinically amyopathic dermatomyositis, in order to facilitate early, accurate diagnosis and appropriate clinical management.

Keywords

Dermatomyositis Clinically amyopathic Hypomyopathic Premyopathic 

Notes

Compliance with Ethics Guidelines

Conflict of Interest

Elizabeth E. Bailey and David F. Fiorentino declare that they have no conflicts of interest.

Human and Animal Rights and Informed Consent

This article does not contain any studies with human or animal subjects performed by any of the authors.

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Copyright information

© Springer Science+Business Media New York 2014

Authors and Affiliations

  1. 1.Department of DermatologyStanford University School of MedicineRedwood CityUSA

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