Current Pain and Headache Reports

, Volume 11, Issue 4, pp 313–316 | Cite as

Red ear syndrome

  • R. Allan Purdy
  • David W. Dodick


The red ear syndrome is a rare syndrome originally described by Lance in 1994. It involves pain in and around the ear and associated autonomic phenomena, the most significant of which is cutaneous erythema of the ear ipsilateral to the pain and obvious to the patient and examiner during the attack. It may well represent an auriculo-autonomic cephalgia and/or be part of the group of disorders recognized as trigeminal autonomic cephalalgias. As a syndrome, it still lacks specificity in regard to etiology, mechanisms, and treatment but is important to recognize clinically because of its associations.


Migraine Cluster Headache Trigeminal Neuralgia Great Auricular Nerve Chronic Paroxysmal Hemicrania 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© Current Medicine Group LLC 2007

Authors and Affiliations

  1. 1.Division of Neurology, Department of MedicineDalhousie University, QEII Health Sciences CenterHalifaxCanada

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