Small Bowel Congenital Anomalies: a Review and Update

Small Intestine (D Sachar, Section Editor)
Part of the following topical collections:
  1. Topical Collection on Small Intestine


The small intestine is a complex organ system that is vital to the life of the individual. There are a number of congenital anomalies that occur and present most commonly in infancy; however, some may not present until adulthood. Most congenital anomalies of the small intestine will present with obstructive symptoms while some may present with vomiting, abdominal pain, and/or gastrointestinal bleeding. Various radiologic procedures can aid in the diagnosis of these lesions that vary depending on the particular anomaly. Definitive therapy for these congenial anomalies is surgical, and in some cases, surgery needs to be performed urgently. The overall prognosis of congenital anomalies of the small intestine is very good and has improved with improved medical management and the advent of newer surgical modalities. The congenital anomalies of the small intestine reviewed in this article include malrotation, Meckel’s diverticulum, duodenal web, duodenal atresia, jejunoileal atresia, and duplications.


Small intestine Small bowel Congenital anomalies Malrotation Meckel’s diverticulum Duodenal web Duodenal atresia Intestinal atresia Jejunoileal atresia Small bowel duplications 


Compliance with Ethical Standards

Conflict of Interest

Grant Morris and Alfred Kennedy Jr. declare that they have no conflicts of interest. William Cochran reports he is on the speaker’s bureau for Nestle Nutrition, outside the submitted work.

Human and Animal Rights and Informed Consent

This article does not contain any studies with human or animal subjects performed by any of the authors.


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Copyright information

© Springer Science+Business Media New York 2016

Authors and Affiliations

  • Grant Morris
    • 1
  • Alfred KennedyJr.
    • 2
  • William Cochran
    • 3
  1. 1.Department of PediatricsGeisinger ClinicDanvilleUSA
  2. 2.Department of Pediatric SurgeryGeisinger ClinicDanvilleUSA
  3. 3.Department of Pediatric GastroenterologyGeisinger ClinicDanvilleUSA

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