Surgery for Portal Hypertension in Children

Article

Abstract

Management of children with portal hypertension has evolved considerably over the past decades. Development of physiologic shunts (meso-Rex bypass) and successful liver transplant has changed the paradigm of portal hypertension surgery. Children with pre-hepatic portal hypertension are investigated and, if suitable, candidates are offered the mesenteric-to-left portal vein bypass (meso-Rex) preemptively, before development of symptoms of portal hypertension. Aggressive medical management, endoscopic ligation of bleeding varices, and radiologically placed intrahepatic stents have greatly reduced the need for emergent surgical procedures. A larger number of surgical options offer a permanent solution for children with portal hypertension in the setting of well-compensated liver function. Portal hypertension in the setting of decompensated liver disease is managed medically (via endoscopy) or radiologically (via transjugular intrahepatic portosystemic shunt) with the aim to offer liver transplant as a permanent solution.

Keywords

Portal hypertension Children Shunts Meso-caval shunt Meso-Rex bypass Selective shunts Nonselective shunts Splenectomy Sugiura procedure 

Notes

Disclosure

Conflicts of interest: S. Scholz—none; K. Sharif—none.

References

Papers of particular interest, published recently, have been highlighted as: • Of importance

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Copyright information

© Springer Science+Business Media, LLC 2011

Authors and Affiliations

  1. 1.Paediatric HPB Surgery and Transplantation, Liver UnitBirmingham Children’s HospitalBirminghamUK

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