Aortic valve replacement for infective endocarditis in an adult with uncorrected tetralogy of Fallot and pulmonary atresia

  • Shuhei TobaEmail author
  • Hisato Ito
  • Ayano Futsuki
  • Naoki Yamamoto
  • Takeshi Konuma
  • Motoshi Takao
  • Yoshito Ogihara
  • Hideto Shimpo
Case Report


Infective endocarditis is one of the complications encountered in patients with uncorrected tetralogy of Fallot; however, there have been only limited reports on surgical treatment of this condition. A 38-year-old man with uncorrected tetralogy of Fallot with pulmonary atresia previously palliated with modified Blalock–Taussig shunt was diagnosed with aortic valve infective endocarditis and developed severe aortic regurgitation. He underwent urgent aortic valve replacement, during which intermittent hypothermic circulatory arrest was necessary to achieve adequate myocardial protection and bloodless surgical field due to massive arterial return into the left ventricle from the collateral pulmonary circulation.


Adult congenital heart disease Infective endocarditis Tetralogy of Fallot with pulmonary atresia Aortic valve replacement Aortopulmonary collateral arteries 



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Copyright information

© The Japanese Association for Thoracic Surgery 2019

Authors and Affiliations

  1. 1.Department of Thoracic and Cardiovascular SurgeryMie University Graduate School of MedicineTsuJapan
  2. 2.Department of Cardiology and NephrologyMie University Graduate School of MedicineTsuJapan

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