General Thoracic and Cardiovascular Surgery

, Volume 65, Issue 4, pp 209–212 | Cite as

A case of staged Norwood procedure for a unique form of truncus arteriosus, interrupted aortic arch with hypoplastic tricuspid valve and right ventricle and anomalous left coronary artery orifice: first reported case

Case Report
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Abstract

We present the first reported case of truncus arteriosus, interrupted aortic arch with hypoplastic tricuspid valve and right ventricle and anomalous left coronary artery orifice in a neonate in whom successful palliation was performed using two-staged procedure. The first-stage palliation was the bilateral pulmonary artery band at age 2 days. The second-stage palliation was a Norwood procedure concomitant with ASD creation and patch augmentation of the pulmonary artery confluence at 22 days. The patient is doing well, with unobstructed aortic arch and mild truncal valve regurgitation.

Keywords

Truncus arteriosus Interrupted aortic arch Hypoplastic right ventricle Hypoplastic tricuspid valve Norwood 
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Notes

Compliance with ethical standards

Conflict of interest

All the authors have declared no competing interest.

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Copyright information

© The Japanese Association for Thoracic Surgery 2015

Authors and Affiliations

  1. 1.Department of the Cardiovascular Surgery, Faculty of MedicineShimane UniversityIzumoJapan
  2. 2.Department of the Pediatric Cardiac Surgery, Faculty of MedicineShimane UniversityIzumoJapan

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