Cor Triatriatum as an Uncommon Cause of Recurrent Syncope
KEY WORDScor triatriatum syncope cardiac anomaly congenital heart disease
Cor triatriatum represents only 0.1–0.4% of congenital cardiac malformations and has several anatomic variants.1,2 Ventricular inflow obstruction results from abnormal septation within the left or right atrium, creating two atrial chambers subdivided by a thin membrane. Many remain asymptomatic until their thirties. Most cases in adulthood are discovered incidentally.3, 4, 5 Clinicians should suspect cor triatriatum in young healthy patients with clinical features mimicking mitral stenosis but no cardiovascular co-morbidities. Early and severe manifestations occur in smaller communicating orifices and higher obstruction between bisected atrial chambers.1 Late symptoms results from progressive increase in pulmonary artery pressure.2 Syncope, heart failure, and sudden cardiac arrest are well cited.5,6 Early diagnosis by echocardiography is important to expedite surgical cure.2,7,8
The authors wish to thank John Petersen, MD for his cardiology expertise and interpretation of the transthoracic echocardiographic images. This case was presented as a clinical vignette poster at the 40th Society of General Internal Medicine Annual Meeting on April 21, 2017.
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Conflict of Interest
The authors declare that they do not have a conflict of interest.
- 1.Cor Triatriatum: Background, Pathophysiology, Epidemiology. Available at: http://emedicine.medscape.com/article/154168-overview#a6. Accessed February 8, 2018
- 3.Mamunur Rashid AKM, Wahab MA, Haque M, Goswami BC. A Rare Congenital Heart Disease – Cor Triatriatum. Int J Case Rep Med 2013;2013:1–7. Article ID 802275. https://doi.org/10.5171/2013.802275