Japanese Journal of Radiology

, Volume 31, Issue 12, pp 775–785

Imaging of vascular tumors with an emphasis on ISSVA classification

  • Taiki Nozaki
  • Masaki Matsusako
  • Hidefumi Mimura
  • Keigo Osuga
  • Mizuko Matsui
  • Hikaru Eto
  • Naoyuki Ohtake
  • Atsushi Manabe
  • Isao Kusakawa
  • Yoshiyuki Tsutsumi
  • Shunsuke Nosaka
  • Minobu Kamo
  • Yukihisa Saida
Pictorial Essay

Abstract

The International Society for the Study of Vascular Anomalies (ISSVA) classification is becoming the international standard classification system for vascular tumors and vascular malformations. The ISSVA classification strictly distinguishes vascular tumors (neoplastic lesions) from vascular malformations (non-neoplastic lesions) based on whether there is a proliferation of vascular endothelial cells present, and it is an extremely useful classification system for determining therapeutic measures. For vascular tumors, it is clinically significant in terms of discriminating infantile hemangioma and rapidly involuting congenital hemangioma, which are expected to spontaneously regress, from other vascular tumors requiring treatment. Needless to say, clinical courses are important for diagnosis, and it is also important for radiologists to understand imaging findings on vascular tumors because such tumors have unique findings on diagnostic images. In this paper, vascular tumors are classified based on the ISSVA classification, and clinical and imaging findings are reviewed.

Keywords

Vascular tumors Hemangioma ISSVA classification 

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Copyright information

© Japan Radiological Society 2013

Authors and Affiliations

  • Taiki Nozaki
    • 1
  • Masaki Matsusako
    • 1
  • Hidefumi Mimura
    • 2
  • Keigo Osuga
    • 3
  • Mizuko Matsui
    • 4
  • Hikaru Eto
    • 5
  • Naoyuki Ohtake
    • 4
  • Atsushi Manabe
    • 6
  • Isao Kusakawa
    • 6
  • Yoshiyuki Tsutsumi
    • 7
  • Shunsuke Nosaka
    • 7
  • Minobu Kamo
    • 1
  • Yukihisa Saida
    • 1
  1. 1.Department of RadiologySt. Luke’s International HospitalTokyoJapan
  2. 2.Department of Diagnostic Radiology 2Kawasaki Hospital, Kawasaki Medical SchoolOkayamaJapan
  3. 3.Department of Diagnostic and Interventional RadiologyOsaka University Graduate School of MedicineSuitaJapan
  4. 4.Department of Plastic Surgery and Reconstructive SurgerySt. Luke’s International HospitalTokyoJapan
  5. 5.Department of DermatologySt. Luke’s International HospitalTokyoJapan
  6. 6.Department of PediatricsSt. Luke’s International Hospital, St. Luke’s International HospitalTokyoJapan
  7. 7.Department of RadiologyNational Center for Child Health and DevelopmentTokyoJapan

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