Japanese Journal of Radiology

, Volume 30, Issue 10, pp 787–797 | Cite as

Congenital lung abnormalities: a pictorial review of imaging findings

  • Fumika Watarai
  • Masashi TakahashiEmail author
  • Takaaki Hosoya
  • Kiyoshi Murata
Pictorial essay


Congenital lung malformations (CLM) comprise a broad spectrum of maldevelopment that spans a continuum of maldevelopment involving parenchyma, bronchi, and vasculature. They may present as respiratory symptoms at birth and can be the source of morbidity and mortality. Early diagnosis is important for adequate therapy to prevent complications, such as recurrent infections, or to help normal lung development. Prenatal diagnosis of CLM using ultrasound (US) and magnetic resonance imaging (MRI) has increased, but chest radiography and computed tomography (CT) still play important roles in making diagnosis. This article reviews the clinical and radiographic features of various CLM.


Congenital lung malformations Computed tomography Chest radiograph 



The authors express their gratitude to Shuhei Inoue, MD, Director and Chief of Department of Thoracic Surgery, National Hospital Organization Shiga Hospital, for his provision of the imaging data of Fig. 3 in this manuscript.


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Copyright information

© Japan Radiological Society 2012

Authors and Affiliations

  • Fumika Watarai
    • 1
    • 2
  • Masashi Takahashi
    • 1
    Email author
  • Takaaki Hosoya
    • 2
  • Kiyoshi Murata
    • 1
  1. 1.Department of RadiologyShiga University of Medical ScienceOtsuJapan
  2. 2.Department of RadiologyYamagata University School of MedicineYamagataJapan

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