, Volume 8, Issue 3, pp 320–323

Dorsal radiocarpal dislocation in a patient with Goldenhar syndrome: case report

  • Johnathan A. Bernard
  • Andres O’Daly
  • Dawn M. LaPorte
Case Reports



Fracture–dislocations of the carpus are rare, generally occurring after high-energy trauma. Goldenhar syndrome is among a group of genetic abnormalities associated with radial limb defects. We present a case of a dorsal radiocarpal dislocation in a patient with Goldenhar syndrome after a low-energy fall. To our knowledge, there has been no previous report of radiocarpal dislocation in the setting of Goldenhar syndrome.


This patient with Goldenhar syndrome had a dorsal radiocarpal dislocation in the setting of an absent scaphoid and dysplastic distal radius. A computed tomography scan, recognized as a useful modality to evaluate the wrist and scaphoid, was used to rule out any other osseous trauma or avulsion fractures.


Closed reduction and 6 weeks of immobilization resulted in a successful treatment.


The incidence of radiocarpal dislocations in patients with Goldenhar syndrome and the appropriate long-term treatment for patients with Goldenhar syndrome with radiocarpal dislocations require further investigation.


Dorsal radiocarpal dislocation Dysplastic distal radius Goldenhar Scaphoid aplasia 


  1. 1.
    Avon SW, Shively JL. Orthopaedic manifestations of Goldenhar syndrome. J Pediatr Orthop. 1988;8:683–6.PubMedCrossRefGoogle Scholar
  2. 2.
    Bush CH, Gillespy III T, Dell PC. High-resolution CT of the wrist: initial experience with scaphoid disorders and surgical fusions. AJR Am J Roentgenol. 1987;149:757–60.PubMedCrossRefGoogle Scholar
  3. 3.
    Dumontier C, Meyer zu Reckendorf G, Sautet A, et al. Radiocarpal dislocations: classification and proposal for treatment. A review of twenty-seven cases. J Bone Joint Surg Am. 2001;83:212–8.PubMedGoogle Scholar
  4. 4.
    Dunn AW. Fractures and dislocations of the carpus. Surg Clin North Am. 1972;52:1513–38.PubMedGoogle Scholar
  5. 5.
    Freund LG, Ovesen J. Isolated dorsal dislocation of the radiocarpal joint. A case report. J Bone Joint Surg Am. 1977;59:277.PubMedGoogle Scholar
  6. 6.
    Ilyas AM, Mudgal CS. Radiocarpal fracture–dislocations. J Am Acad Orthop Surg. 2008;16:647–55.PubMedGoogle Scholar
  7. 7.
    Moneim MS, Bolger JT, Omer GE. Radiocarpal dislocation—classification and rationale for management. Clin Orthop Relat Res. 1985;192:199–209.PubMedGoogle Scholar
  8. 8.
    Taleisnik J. Current concepts review. Carpal instability. J Bone Joint Surg Am. 1988;70:1262–8.PubMedGoogle Scholar
  9. 9.
    Touliatou V, Fryssira H, Mavrou A, et al. Clinical manifestations in 17 Greek patients with Goldenhar syndrome. Genet Couns. 2006;17:359–70.PubMedGoogle Scholar
  10. 10.
    Vendramini S, Richieri-Costa A, Guion-Almeida ML. Oculoauriculovertebral spectrum with radial defects: a new syndrome or an extension of the oculoauriculovertebral spectrum? Report of fourteen Brazilian cases and review of the literature. Eur J Hum Genet. 2007;15:411–21.PubMedCrossRefGoogle Scholar

Copyright information

© American Association for Hand Surgery 2013

Authors and Affiliations

  • Johnathan A. Bernard
    • 1
  • Andres O’Daly
    • 1
  • Dawn M. LaPorte
    • 1
    • 2
  1. 1.Division of Hand and Upper Extremity Surgery, Department of Orthopaedic SurgeryThe Johns Hopkins UniversityBaltimoreUSA
  2. 2.c/o Elaine P. Henze, BJ, ELS, Medical Editor and Director, Editorial Services, Department of Orthopaedic SurgeryThe Johns Hopkins University/Johns Hopkins Bayview Medical CenterBaltimoreUSA

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