Gorham’s disease of the mandible: radiological features
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The most conspicuous element of Gorham’s disease is its radiographic features, wherein massive disappearance of the mandible is observed. We report a case of an adolescent boy with massive osteolysis of the mandible in whom the diagnosis of Gorham’s disease was made. A 14-year-old boy was referred to the Department of Oral and Maxillofacial Surgery, Universiti Kebangsaan Malaysia Medical Centre, Kuala Lumpur, for the management of a massive mandibular deformity. He was diagnosed with a hemangioma-like lesion at 1 year of age. The disease had progressed for an unknown number of years. Plain X-rays and computed tomography images were examined for reconstructive surgery planning. Gorham’s disease is self-limiting, but has catastrophic results. The role of imaging is huge, particularly for reconstructive surgery planning.
KeywordsGorham’s disease Radiological features Mandible
We thank Dr. Kew Thean Yean, Department of Radiology, Universiti Kebangsaan Malaysia Medical Centre for his help with the imaging.
Compliance with ethical standards
Conflict of interest
Hui Yuh Soh, Azizah Ahmad, Abd Jabar Nazimi, and Roszalina Ramli declare that they have no conflict of interest.
Human rights statements
All procedures followed were in accordance with the ethical standards of the responsible committee on human experimentation (institutional and national) and with the Helsinki Declaration of 1964 and later versions.
Informed consent was obtained from the patient (now aged above 21 years) for being included in the study.
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