, Volume 8, Issue 2, pp 109–114 | Cite as

Sellar Neuroblastoma Mimicking Pituitary Adenoma

  • Ken-ichi OyamaEmail author
  • Shozo Yamada
  • Masaaki Usui
  • Kalman Kovacs


Objective and importance: Primary intracranial neuroblastomas are rare. They generally arise in the supratentorial parenchyma or paraventricular region. Even more rare are primary sellar neuroblastomas. We present a neuroblastoma that arose in the sellar region and mimicked a non-functioning pituitary adenoma. Clinical presentation: This 33-year-old man presented with bitemporal hemianopsia. MRI showed a sellar mass with suprasellar extension mimicking a pituitary adenoma. Intervention: Because of tumor recurrence and dissemination to the cervical region, he underwent 6 operations and radiosurgery. Detailed histologic examination confirmed the diagnosis of neuroblastoma. Postoperative conventional radiotherapy was effective in reducing the size of the tumor. Conclusion: Neuroblastoma should be considered in the differential diagnosis of patients with sellar lesions.

Key Words

neuroblastoma pituitary tumors sellar lesions sella turcica radiotherapy 


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Copyright information

© Springer Science + Business Media, Inc. 2005

Authors and Affiliations

  • Ken-ichi Oyama
    • 1
    • 3
    Email author
  • Shozo Yamada
    • 1
  • Masaaki Usui
    • 2
  • Kalman Kovacs
    • 2
  1. 1.Department of Hypothalamic & Pituitary SurgeryToranomon HospitalMinato-kuJapan
  2. 2.Department of NeurosurgeryToranomon HospitalMinato-kuJapan
  3. 3.Department of Hypothalamic & Pituitary SurgeryToranomon HospitalMinato-kuJapan

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